PEPD

Management

The following evaluations are recommended:

  • Supportive treatment of skin, lung, and immunologic manifestations
  • Developmental and educational interventions as needed to address motor and cognitive delays
  • Immunization and antibiotic treatment at the first sign of infection for patients who have undergone splenectomy
  • Antibiotic prophylaxis in the appropriate setting
  • Complete blood count and liver function tests
  • Abdominal ultrasound examination to assess the size of the liver and spleen