Patient Overview : 12

General

Frequency of all clinical findings

Percentage Cases
Gender    
Male 58.3% 7/12
Female 41.7% 5/12
Indifferent 0% 0/12
Unknown 0% 0/12
General    
Birth Length abnormalities 16.7% 2/12
< P3 : Birth length less than 3rd percentile 16.7% 2/12
Birth Weight abnormalities 16.7% 2/12
< P3 : Small for gestational age 16.7% 2/12
Birth Head circumference abnormalities 8.3% 1/12
< P3 : Primary microcephaly 8.3% 1/12
Current Height abnormalities 8.3% 1/12
< P3 : Short stature 8.3% 1/12
Current Weight abnormalities 33.3% 4/12
< P3 : Decreased body weight 16.7% 2/12
> P98 : Increased body weight 16.7% 2/12
Current Head circumference abnormalities 16.7% 2/12
< P3 : Microcephaly 8.3% 1/12
> P98 : Macrocephaly 8.3% 1/12
Neurology    
Neurological abnormalities 100.0% 10/10
Generalized hypotonia 70.0% 7/10
Failure to thrive 20.0% 2/10
Abnormality of the musculature of the upper limbs 10.0% 1/10
Autism 10.0% 1/10
Bilateral tonic-clonic seizure 10.0% 1/10
Febrile seizure (within the age range of 3 months to 6 years) 10.0% 1/10
Frequent falls 10.0% 1/10
Gait ataxia 10.0% 1/10
Language impairment 10.0% 1/10
Spasticity 10.0% 1/10
Behavioral problems 100.0% 5/5
Abnormal sexual behavior 20.0% 1/5
Aggressive behavior 20.0% 1/5
Attention deficit hyperactivity disorder 20.0% 1/5
Autistic behavior 20.0% 1/5
Hyperactivity 20.0% 1/5
Impulsivity 20.0% 1/5
obsolete Mood swings 20.0% 1/5
Short attention span 20.0% 1/5
Sleep disturbance 20.0% 1/5
Brain abnormality 57.1% 4/7
Abnormal cerebral white matter morphology 28.6% 2/7
Abnormal cerebellar vermis morphology 14.3% 1/7
Abnormal corpus callosum morphology 14.3% 1/7
Abnormal lateral ventricle morphology 14.3% 1/7
Abnormal left ventricle morphology 14.3% 1/7
Abnormal brainstem morphology 14.3% 1/7
Occipital cortical atrophy 14.3% 1/7
Retrocerebellar cyst 14.3% 1/7
Facial abnormalities    
Abnormality of the ear 100.0% 9/9
Low-set ears 66.7% 6/9
Cupped ear 11.1% 1/9
Hypoplastic helices 11.1% 1/9
Large earlobe 11.1% 1/9
Macrotia 11.1% 1/9
Microtia 11.1% 1/9
obsolete Low-set, posteriorly rotated ears 11.1% 1/9
Posteriorly rotated ears 11.1% 1/9
Abnormality of the eye 100.0% 12/12
Abnormality of the eye 108.3% 13/12
Upslanted palpebral fissure 75.0% 9/12
Deeply set eye 50.0% 6/12
Long eyelashes 41.7% 5/12
Strabismus 33.3% 4/12
Abnormal eyebrow morphology 25.0% 3/12
obsolete Sparse and thin eyebrow 25.0% 3/12
Thick eyebrow 25.0% 3/12
Hypertelorism 16.7% 2/12
Synophrys 16.7% 2/12
Blepharophimosis 8.3% 1/12
Downslanted palpebral fissures 8.3% 1/12
Exotropia 8.3% 1/12
Highly arched eyebrow 8.3% 1/12
Hypotelorism 8.3% 1/12
Short palpebral fissure 8.3% 1/12
Abnormality of the nose 100.0% 10/10
Anteverted nares 60.0% 6/10
Triangular nasal tip 50.0% 5/10
Abnormal nasal bridge morphology 20.0% 2/10
Low hanging columella 20.0% 2/10
Abnormal columella morphology 10.0% 1/10
Abnormal morphology of the nasal alae 10.0% 1/10
Depressed nasal bridge 10.0% 1/10
Flared nostrils 10.0% 1/10
Prominent nose 10.0% 1/10
Short nose 10.0% 1/10
Short columella 10.0% 1/10
Wide nasal base 10.0% 1/10
Abnormality of the mouth 100.0% 12/12
Micrognathia 66.7% 8/12
Thin upper lip vermilion 33.3% 4/12
Smooth philtrum 25.0% 3/12
Wide mouth 25.0% 3/12
Downturned corners of mouth 16.7% 2/12
High palate 16.7% 2/12
Long philtrum 16.7% 2/12
Tooth malposition 16.7% 2/12
Absent cupid's bow 8.3% 1/12
Cleft palate 8.3% 1/12
Dental malocclusion 8.3% 1/12
Mandibular prognathia 8.3% 1/12
Oligodontia 8.3% 1/12
Open bite 8.3% 1/12
Thin lower lip vermilion 8.3% 1/12
Visual and hearing impairments    
Abnormal hearing 100.0% 1/1
Sensorineural hearing impairment 100.0% 1/1
Abnormal vision 66.7% 2/3
Hypertelorism 33.3% 1/3
Hyperopic astigmatism 33.3% 1/3
Heart    
Abnormality of the heart 100.0% 3/3
Abnormal aortic valve morphology 33.3% 1/3
Aortic regurgitation 33.3% 1/3
Pulmonic stenosis 33.3% 1/3
Pulmonary    
Abnormality of the lungs 100.0% 3/3
Bronchiolitis 33.3% 1/3
Pulmonic stenosis 33.3% 1/3
Recurrent respiratory infections 33.3% 1/3
Sleep apnea 33.3% 1/3
Gastrointestinal    
Gastrointestinal abnormalities 100.0% 4/4
Abnormality of the genitourinary system 25.0% 1/4
Gastroesophageal reflux 25.0% 1/4
Pyelonephritis 25.0% 1/4
Urinary bladder sphincter dysfunction 25.0% 1/4
Vomiting 25.0% 1/4
Urogenital    
Abnormality of the urogenital system 100.0% 2/2
Abnormal renal corticomedullary differentiation 50.0% 1/2
Hyperechogenic kidneys 50.0% 1/2
Renal insufficiency 50.0% 1/2
Renal cyst 50.0% 1/2
Unilateral cryptorchidism 50.0% 1/2
Skeleton    
Skeletal abnormalities 100.0% 12/12
Scoliosis 50.0% 6/12
Brachydactyly 16.7% 2/12
Broad hallux 16.7% 2/12
Pes planus 16.7% 2/12
Short finger 16.7% 2/12
2-3 toe syndactyly 16.7% 2/12
Abnormal sacral segmentation 8.3% 1/12
Abnormal finger morphology 8.3% 1/12
Abnormal fingertip morphology 8.3% 1/12
Abnormal Achilles tendon morphology 8.3% 1/12
Abnormal pelvis bone morphology 8.3% 1/12
Abnormality of the knee 8.3% 1/12
Abnormality of the lower limb 8.3% 1/12
Abnormal occipital bone morphology 8.3% 1/12
Brachycephaly 8.3% 1/12
Clinodactyly of the 4th toe 8.3% 1/12
Joint hypermobility 8.3% 1/12
Juvenile rheumatoid arthritis 8.3% 1/12
Kyphosis 8.3% 1/12
Limited elbow extension 8.3% 1/12
Narrow chest 8.3% 1/12
obsolete Joint laxity 8.3% 1/12
Pectus excavatum 8.3% 1/12
Pseudohypoparathyroidism 8.3% 1/12
Short neck 8.3% 1/12
Slender finger 8.3% 1/12
Skin / Hair / Nails    
Abnormality of the skin/hair/nails 100.0% 7/7
Supernumerary nipple 28.6% 2/7
Abnormal finger morphology 14.3% 1/7
Brachydactyly 14.3% 1/7
Deep palmar crease 14.3% 1/7
Hirsutism 14.3% 1/7
Hyperextensible skin 14.3% 1/7
Low anterior hairline 14.3% 1/7
Pterygium 14.3% 1/7
Redundant skin 14.3% 1/7
Sacrococcygeal pilonidal abnormality 14.3% 1/7
Single transverse palmar crease 14.3% 1/7
Tapered finger 14.3% 1/7
Endocrine / Immunological / Metabolic    
Abnormality of the metabolic system 100.0% 2/2
Abnormal circulating creatine kinase concentration 50.0% 1/2
Hypercalcemia 50.0% 1/2
Abnormality of the immune system 42.9% 3/7
Elevated circulating thyroid-stimulating hormone concentration 14.3% 1/7
Hypothyroidism 14.3% 1/7
Recurrent infections 14.3% 1/7