FGD1

Clinical Characteristics

Prenatal findings
•    intra-uterine growth retardation
•    short limbs
•    short tubular bones
•    equinovarus clubfeet
•    other feet malposition

Post-natal growth
•    low birth length
•    short stature
•    short limbs
•    growth hormone deficiency
•    growth hormone treatment

Craniofacial features
•    broad forehead
•    widow’s peak or fontal upswift
•    hypertelorism
•    broad eyebrows
•    sparse eyebrows
•    down-slanting palpebral fissures
•    ptosis
•    broad nasal bridge
•    short nose
•    anteverted nares
•    flat face
•    wide philtrum
•    long philtrum
•    thin upper lip
•    wavy mouth when smiling
•    everted lower lip
•    linear dimple below the lower lip
•    low-set posteriorly rotated ears
•    small ears
•    thick rectangular antitragus

Limb and skeletal anomalies
•    short hands
•    broad hands
•    brachydactylies
•    camptodactylies
•    cutaneous syndactylies
•    single palmar creases
•    single flexion crease of the 5th fingers
•    swan neck deformity of the fingers
•    broad proximal interphalangeal joints of the hands
•    short feet
•    broad feet
•    short toes
•    bulbous tip of the feet
•    metatarsus varus
•    equinovarus club feet
•    other feet malposition
•    brachymelia
•    short and large neck
•    pectus excavatum
•    scoliosis
•    joint hyperlaxity
•    osteochondritis

Other morphological features
•    shawl scrotum
•    umbilicus abnormalities

Congenital malformations
•    cryptorchidism
•    micropenis
•    hypospadias
•    inguinal hernia
•    heart defect
•    aortic dilatation
•    cleft lip/palate
•    anal anomalies (anus imperforate, anal stenosis or anterior placement)
•    brain malformation
•    cerebral vascular dysplasia

Other medical problems
•    dental anomalies
•    hyperopia
•    strabismus
•    astigmatism

Neurological features – neurodevelopment disorders
•    neonatal hypotonia
•    childhood hypotonia
•    delayed motors skills
•    delayed language

•    learning difficulties

•    special needs education
•    ADHD
•    specific learning disorders (dyslexia, dysgraphia, dyscalculia …
•    intellectual disability
•    myopathic features (muscle pain, exercise intolerance)

Radiological features
•    short metacarpals
•    short distal phalanges
•    brachymesophalangia of the 5th fingers
•    broad 1rst metacarpals
•    broad and short 5th metacarpals
•    cone-shaped epiphyses
•    short metatarsals
•    broad 1rst metatarsals
•    short and broad femoral necks
•    small femoral epiphyses
•    coxa valga
•    broad inner parts of the clavicles
•    short long bones
•    delayed bone age
•    enlarged metaphyses
•    narrow vertebral canal
•    vertebral anomalies
•    cervical spine anomalies