Patient Overview : 41

General

Frequency of all clinical findings

Percentage Cases
Gender    
Male 43.9% 18/41
Female 56.1% 23/41
General    
Birth Length abnormalities 20.7% 6/29
< P3 : Birth length less than 3rd percentile 13.8% 4/29
> P98 : Birth length greater than 97th percentile 6.9% 2/29
Birth Weight abnormalities 30.0% 9/30
< P3 : Small for gestational age 30.0% 9/30
Birth Head circumference abnormalities 17.9% 5/28
< P3 : Primary microcephaly 14.3% 4/28
> P98 : Macrocephaly at birth 3.6% 1/28
Current Height abnormalities 10.0% 3/30
< P3 : Short stature 10.0% 3/30
Current Weight abnormalities 16.1% 5/31
> P98 : Increased body weight 9.7% 3/31
< P3 : Decreased body weight 6.5% 2/31
Current Head circumference abnormalities 17.2% 5/29
> P98 : Macrocephaly 13.8% 4/29
< P3 : Microcephaly 3.4% 1/29
Neurology    
Neurological abnormalities 82.1% 32/39
Hypotonia 38.5% 15/39
Absent speech 20.5% 8/39
Seizure 15.4% 6/39
Inability to walk 10.3% 4/39
Gait ataxia 7.7% 3/39
Ataxia 5.1% 2/39
Axial hypotonia 5.1% 2/39
Generalized hypotonia 5.1% 2/39
Intellectual disability 5.1% 2/39
Limb hypertonia 5.1% 2/39
Moderate global developmental delay 5.1% 2/39
Muscle weakness 5.1% 2/39
Neurodevelopmental delay 5.1% 2/39
Postural instability 5.1% 2/39
Abnormality of coordination 2.6% 1/39
Broad-based gait 2.6% 1/39
Chorea 2.6% 1/39
Delayed fine motor development 2.6% 1/39
Delayed speech and language development 2.6% 1/39
Dystonia 2.6% 1/39
Febrile seizure (within the age range of 3 months to 6 years) 2.6% 1/39
Gait disturbance 2.6% 1/39
Generalized non-motor (absence) seizure 2.6% 1/39
Global developmental delay 2.6% 1/39
Language impairment 2.6% 1/39
Neonatal hypotonia 2.6% 1/39
Neurodevelopmental abnormality 2.6% 1/39
Nystagmus 2.6% 1/39
obsolete Infantile axial hypotonia 2.6% 1/39
obsolete Poor coordination 2.6% 1/39
Severe muscular hypotonia 2.6% 1/39
Spasticity 2.6% 1/39
Spastic paraparesis 2.6% 1/39
Speech apraxia 2.6% 1/39
Behavioral problems 35.9% 14/39
Aggressive behavior 7.7% 3/39
Autism 7.7% 3/39
Autistic behavior 5.1% 2/39
Motor stereotypy 5.1% 2/39
Abnormal drinking behavior 2.6% 1/39
Abnormal eating behavior 2.6% 1/39
Anxiety 2.6% 1/39
Compulsive behaviors 2.6% 1/39
Delayed speech and language development 2.6% 1/39
Hyperactivity 2.6% 1/39
Inappropriate laughter 2.6% 1/39
obsolete Abnormal aggressive, impulsive or violent behavior 2.6% 1/39
Polyphagia 2.6% 1/39
Self-mutilation 2.6% 1/39
Skin-picking 2.6% 1/39
Sleep disturbance 2.6% 1/39
Brain abnormality 50.0% 15/30
Abnormal cerebral white matter morphology 6.7% 2/30
Cerebral hypomyelination 6.7% 2/30
Ventriculomegaly 6.7% 2/30
Cavum septum pellucidum 3.3% 1/30
Cerebral white matter hypoplasia 3.3% 1/30
Cerebral atrophy 3.3% 1/30
Cerebral cortical atrophy 3.3% 1/30
Cystic lesions of the pinnae 3.3% 1/30
Dandy-Walker malformation 3.3% 1/30
Delayed myelination 3.3% 1/30
Dilation of Virchow-Robin spaces 3.3% 1/30
Hypoplasia of the corpus callosum 3.3% 1/30
Lateral ventricle dilatation 3.3% 1/30
Lateral ventricular asymmetry 3.3% 1/30
Partial agenesis of the corpus callosum 3.3% 1/30
Polymicrogyria 3.3% 1/30
Punctate periventricular T2 hyperintense foci 3.3% 1/30
Facial abnormalities    
Abnormality of the ear 42.5% 17/40
Low-set ears 22.5% 9/40
Large fleshy ears 7.5% 3/40
Abnormal earlobe morphology 5.0% 2/40
Anteverted ears 5.0% 2/40
Preauricular pit 5.0% 2/40
Large earlobe 2.5% 1/40
Macrotia 2.5% 1/40
Prominent ear helix 2.5% 1/40
Prominent antihelix 2.5% 1/40
Abnormality of the eye 62.5% 25/40
Upslanted palpebral fissure 25.0% 10/40
Horizontal eyebrow 15.0% 6/40
Long eyelashes 15.0% 6/40
Epicanthus 12.5% 5/40
Downslanted palpebral fissures 5.0% 2/40
Esotropia 5.0% 2/40
Synophrys 5.0% 2/40
Abnormal eyelid morphology 2.5% 1/40
Bilateral microphthalmos 2.5% 1/40
Bilateral ptosis 2.5% 1/40
Blepharophimosis 2.5% 1/40
Epicanthus inversus 2.5% 1/40
Highly arched eyebrow 2.5% 1/40
Hypertelorism 2.5% 1/40
Hyperopic astigmatism 2.5% 1/40
Hypotelorism 2.5% 1/40
obsolete Prominent epicanthal folds 2.5% 1/40
Ptosis 2.5% 1/40
Short palpebral fissure 2.5% 1/40
Strabismus 2.5% 1/40
Telecanthus 2.5% 1/40
Unilateral ptosis 2.5% 1/40
Abnormality of the nose 67.5% 27/40
Prominent nasal tip 27.5% 11/40
Deep philtrum 22.5% 9/40
Bulbous nose 17.5% 7/40
Depressed nasal bridge 17.5% 7/40
Abnormal external nose morphology 2.5% 1/40
Low hanging columella 2.5% 1/40
Prominent nose 2.5% 1/40
Short nose 2.5% 1/40
Short philtrum 2.5% 1/40
Wide nose 2.5% 1/40
Wide nasal bridge 2.5% 1/40
Abnormality of the mouth 80.0% 32/40
Open mouth 42.5% 17/40
Exaggerated cupid's bow 20.0% 8/40
Macroglossia 15.0% 6/40
Thin vermilion border 10.0% 4/40
Wide mouth 10.0% 4/40
Mandibular prognathia 7.5% 3/40
Protruding tongue 7.5% 3/40
Short philtrum 7.5% 3/40
Thin upper lip vermilion 7.5% 3/40
Deep philtrum 5.0% 2/40
Retrognathia 5.0% 2/40
Abnormal upper lip morphology 2.5% 1/40
Ankyloglossia 2.5% 1/40
Drooling 2.5% 1/40
High forehead 2.5% 1/40
Movement abnormality of the tongue 2.5% 1/40
Narrow forehead 2.5% 1/40
Thick vermilion border 2.5% 1/40
Visual and hearing impairments    
Abnormal hearing 10.3% 4/39
Conductive hearing impairment 2.6% 1/39
Hearing impairment 2.6% 1/39
Mild conductive hearing impairment 2.6% 1/39
Abnormal vision 35.9% 14/39
Astigmatism 12.8% 5/39
Hypermetropia 7.7% 3/39
Strabismus 7.7% 3/39
Myopia 5.1% 2/39
Alternating esotropia 2.6% 1/39
Duane anomaly 2.6% 1/39
High hypermetropia 2.6% 1/39
Hyperopic astigmatism 2.6% 1/39
Monocular strabismus 2.6% 1/39
Ptosis 2.6% 1/39
Heart    
Abnormality of the heart 20.0% 8/40
Tetralogy of Fallot 7.5% 3/40
Patent foramen ovale 5.0% 2/40
Pulmonary valve atresia 5.0% 2/40
Ventricular septal defect 5.0% 2/40
Cardiac total anomalous pulmonary venous connection 2.5% 1/40
Primum atrial septal defect 2.5% 1/40
Supracardiac total anomalous pulmonary venous connection 2.5% 1/40
Pulmonary    
Abnormality of the lungs 23.1% 3/13
Recurrent bronchitis 7.7% 1/13
Gastrointestinal    
Gastrointestinal abnormalities 17.5% 7/40
Gastroesophageal reflux 5.0% 2/40
Abdominal pain 2.5% 1/40
Anteriorly placed anus 2.5% 1/40
Constipation 2.5% 1/40
Enterocolitis 2.5% 1/40
Meckel diverticulum 2.5% 1/40
Urogenital    
Abnormality of the urogenital system 17.5% 7/40
Abnormal testis morphology 2.5% 1/40
Abnormality of the kidney 2.5% 1/40
Glanular hypospadias 2.5% 1/40
Hydroureter 2.5% 1/40
Unilateral cryptorchidism 2.5% 1/40
Ureter duplex 2.5% 1/40
Urinary incontinence 2.5% 1/40
Skeleton    
Skeletal abnormalities 62.5% 25/40
Brachycephaly 10.0% 4/40
Bilateral talipes equinovarus 7.5% 3/40
Lumbar hyperlordosis 7.5% 3/40
Talipes equinovarus 7.5% 3/40
Metatarsus adductus 5.0% 2/40
Overlapping toe 5.0% 2/40
Sandal gap 5.0% 2/40
Tapered finger 5.0% 2/40
Bowing of the legs 2.5% 1/40
Camptodactyly of finger 2.5% 1/40
Clinodactyly of hallux 2.5% 1/40
Clinodactyly of the 2nd toe 2.5% 1/40
Clinodactyly 2.5% 1/40
Congenital foot contraction deformities 2.5% 1/40
Craniosynostosis 2.5% 1/40
Cubitus valgus 2.5% 1/40
Hip contracture 2.5% 1/40
Joint hypermobility 2.5% 1/40
Kyphoscoliosis 2.5% 1/40
Long toe 2.5% 1/40
Proximal placement of thumb 2.5% 1/40
Scoliosis 2.5% 1/40
Spinal canal stenosis 2.5% 1/40
Thumb contracture 2.5% 1/40
Toe clinodactyly 2.5% 1/40
3-5 toe syndactyly 2.5% 1/40
Skin / Hair / Nails    
Abnormality of the skin/hair/nails 20.0% 8/40
Crusting erythematous dermatitis 2.5% 1/40
Eczematoid dermatitis 2.5% 1/40
High forehead 2.5% 1/40
Inguinal hernia 2.5% 1/40
Nevus 2.5% 1/40
Supernumerary nipple 2.5% 1/40
Sydney crease 2.5% 1/40
Thick hair 2.5% 1/40
Endocrine / Immunological / Metabolic    
Abnormality of the immune system 2.5% 1/40
Recurrent herpes 2.5% 1/40
Neoplasia    
Neoplasia 7.5% 3/40
Acute lymphoblastic leukemia 5.0% 2/40