Patient Overview : 20

General

Frequency of all clinical findings

Percentage Cases
Gender    
Male 35.0% 7/20
Female 65.0% 13/20
General    
Birth Length abnormalities 15.0% 3/20
< P3 : Birth length less than 3rd percentile 10.0% 2/20
> P98 : Birth length greater than 97th percentile 5.0% 1/20
Birth Weight abnormalities 30.0% 6/20
< P3 : Small for gestational age 30.0% 6/20
Birth Head circumference abnormalities 15.0% 3/20
< P3 : Congenital microcephaly 15.0% 3/20
Current Height abnormalities 30.0% 6/20
< P3 : Short stature 25.0% 5/20
> P98 : Tall stature 5.0% 1/20
Current Weight abnormalities 30.0% 6/20
< P3 : Decreased body weight 25.0% 5/20
> P98 : Increased body weight 5.0% 1/20
Current Head circumference abnormalities 35.0% 7/20
< P3 : Microcephaly 30.0% 6/20
> P98 : Macrocephaly 5.0% 1/20
Neurology    
Neurological abnormalities 93.8% 15/16
Dysarthria 43.8% 7/16
EEG abnormality 43.8% 7/16
Seizures 25.0% 4/16
Absent speech 12.5% 2/16
Cerebral palsy 12.5% 2/16
Focal seizures 12.5% 2/16
Gait ataxia 12.5% 2/16
Hyperreflexia 12.5% 2/16
Absence seizures 6.3% 1/16
Autism 6.3% 1/16
Broad-based gait 6.3% 1/16
Epileptic encephalopathy 6.3% 1/16
Expressive language delay 6.3% 1/16
Inability to walk 6.3% 1/16
Receptive language delay 6.3% 1/16
Spastic diplegia 6.3% 1/16
Spasticity 6.3% 1/16
Speech apraxia 6.3% 1/16
Status epilepticus 6.3% 1/16
Stereotypic behavior 6.3% 1/16
Tremor 6.3% 1/16
Behavioral problems 100.0% 3/3
Aggressive behavior 33.3% 1/3
Emotional lability 33.3% 1/3
Impulsivity 33.3% 1/3
Self-injurious behavior 33.3% 1/3
Brain abnormality 46.2% 6/13
Abnormality of the periventricular white matter 15.4% 2/13
Abnormal cortical gyration 7.7% 1/13
Cerebral atrophy 7.7% 1/13
Periventricular leukomalacia 7.7% 1/13
Ventriculomegaly 7.7% 1/13
Facial abnormalities    
Abnormality of the ear 100.0% 4/4
Abnormality of the outer ear 25.0% 1/4
Abnormality of the pinna 25.0% 1/4
Abnormality of the Eustachian tube 25.0% 1/4
Asymmetry of the ears 25.0% 1/4
Low-set ears 25.0% 1/4
Abnormality of the eye 100.0% 3/3
Astigmatism 33.3% 1/3
Downslanted palpebral fissures 33.3% 1/3
Epicanthus 33.3% 1/3
Prominent epicanthal folds 33.3% 1/3
Telecanthus 33.3% 1/3
Upslanted palpebral fissure 33.3% 1/3
Abnormality of the nose 100.0% 4/4
Depressed nasal bridge 50.0% 2/4
Abnormality of the columella 25.0% 1/4
Anteverted nares 25.0% 1/4
Bulbous nose 25.0% 1/4
Wide nasal bridge 25.0% 1/4
Abnormality of the mouth 100.0% 5/5
Widely spaced teeth 40.0% 2/5
Abnormality of the teeth 20.0% 1/5
Dental malocclusion 20.0% 1/5
Macrodontia 20.0% 1/5
Macroglossia 20.0% 1/5
Protruding tongue 20.0% 1/5
Thin upper lip vermilion 20.0% 1/5
Wide mouth 20.0% 1/5
Visual and hearing impairments    
Abnormal vision 90.0% 9/10
Strabismus 50.0% 5/10
Exotropia 30.0% 3/10
Astigmatism 10.0% 1/10
Congenital strabismus 10.0% 1/10
Esotropia 10.0% 1/10
Hypermetropia 10.0% 1/10
Nystagmus 10.0% 1/10
Heart    
Abnormality of the heart 100.0% 1/1
Abnormality of the aorta 100.0% 1/1
Abnormality of the left ventricle 100.0% 1/1
Pulmonary    
Abnormality of the lungs 100.0% 1/1
Recurrent pneumonia 100.0% 1/1
Gastrointestinal    
Gastrointestinal abnormalities 73.3% 11/15
Feeding difficulties 33.3% 5/15
Constipation 26.7% 4/15
Gastroesophageal reflux 20.0% 3/15
Dysphagia 6.7% 1/15
Esophagitis 6.7% 1/15
Esophageal stenosis 6.7% 1/15
Growth delay 6.7% 1/15
Hiatus hernia 6.7% 1/15
Tracheoesophageal fistula 6.7% 1/15
Weight loss 6.7% 1/15
Urogenital    
Abnormality of the urogenital system 47.1% 8/17
Abnormality of the genitourinary system 52.9% 9/17
Hydronephrosis 11.8% 2/17
Urinary incontinence 11.8% 2/17
Ambiguous genitalia 5.9% 1/17
Anal atresia 5.9% 1/17
Aplasia of the bladder 5.9% 1/17
Cloacal abnormality 5.9% 1/17
Cryptorchidism 5.9% 1/17
Cystic renal dysplasia 5.9% 1/17
Enuresis 5.9% 1/17
Hematuria 5.9% 1/17
Recurrent urinary tract infections 5.9% 1/17
Unilateral cryptorchidism 5.9% 1/17
Skeleton    
Skeletal abnormalities 62.5% 5/8
Congenital contracture 12.5% 1/8
Dislocated radial head 12.5% 1/8
Hip contracture 12.5% 1/8
Increased anterioposterior diameter of thorax 12.5% 1/8
Joint laxity 12.5% 1/8
Scoliosis 12.5% 1/8
Talipes equinovarus 12.5% 1/8
Thoracolumbar scoliosis 12.5% 1/8
Skin / Hair / Nails    
Abnormality of the skin/hair/nails 100.0% 4/4
Extension of eyebrows towards upper eyelid 25.0% 1/4
Long eyelashes 25.0% 1/4
Sparse eyebrow 25.0% 1/4
Synophrys 25.0% 1/4
Endocrine / Immunological / Metabolic    
Abnormality of the endocrine system 100.0% 2/2
Abnormality of the anterior pituitary 50.0% 1/2
Adrenocortical abnormality 50.0% 1/2
Central hypothyroidism 50.0% 1/2
Delayed puberty 50.0% 1/2
Growth hormone deficiency 50.0% 1/2
Hyperthyroidism 50.0% 1/2
Hypogonadotrophic hypogonadism 50.0% 1/2
Abnormality of the metabolic system 33.3% 1/3
Hypoglycemia 33.3% 1/3