ADGRG6

Molecular characteristics

All cases to date have had bi-allelic variants, including nonsense and essential splice site variants which are considered as null alleles. In one case with a homozygous missense change, cell culture studies showed that the substituted amino acid resulted in an inability for the mutant protein to undergo autolytic cleavage, thus the active/shortened form of the protein was not made – thus this case was considered a functional null.