DDX59

Clinical Characteristics

Mutations in the DDX59 gene may cause the following signs and symptoms:

  • Cleft palate (defect of the roof of the mouth manifested as an abnormal ‘opening’ or a ‘split’)
  • Cleft lip (defect of the lips manifested as an abnormal ‘opening’ or a ‘split’)
  • Bifid uvula (split in the uvula, the piece of flesh at the back of the mouth)
  • Lobulated tongue
  • Multiple oral frenula (folds of tissue the connects the tongue to the floor of the mouth and the lips to the gums)
  • Facial dysmorphia, including prominence of the forehead and increased distance between the eyes
  • Possession of extra fingers or toes
  • Intellectual disability
  • Seizures
  • Floppy limbs
  • Developmental delay

Some patients may have:

  • Heart anomalies
  • Scoliosis (sideways curvature of the spine)
  • Fused kidneys
  • Defect in the formation of corpus callosum (the part that connects the two hemispheres of the brain)
  • Hirschsprung disease (blockage of the intestines)