FBXL4

Clinical Characteristics

Mutations in FBXL4 gene may cause the following signs and symptoms:

  • Weak muscle tone (hypotonia)
  • Brain dysfunction (encephalopathy)
  • Failure to grow or gain weight at the expected rate
  • Delayed motor skills development
  • Movement abnormalities
  • Impaired speech development
  • Seizures
  • Microcephaly (smaller-than-normal head)
  • Unusual facial features (including broad nasal bridge, a long space between the upper lip and nose, and thick eyebrows)
  • Abnormal findings on brain MRI imaging
  • Congenital heart defects
  • Heart rhythm abnormalities
  • Vision problems
  • Hearing loss
  • Immune deficiency
  • Liver disease
  • Build-up of a chemical called lactic acid in the body (lactic acidosis)
  • Build-up of ammonia in the blood