RIC1

Clinical Characteristics

CATIFA syndrome, associated with mutations in the RIC1 gene, manifests through a variety of clinical features observed among the 8 known cases reported to date. The symptoms include:

•    Craniofacial anomalies:
o    Elongated face (8/8)
o    Short, broad upturned nose with anteverted nares (8/8)
o    Long philtrum (8/8)
o    Cleft lip/palate (5/8)
o    Microcephaly (4/8)


•    Dental issues:
o    Tooth eruption and alignment deficits (8/8)
o    Extensive caries (8/8)

•    Neurological symptoms:
o    Global developmental delay (8/8)
o    Intellectual disability (8/8)
o    Motor, speech, and cognitive deficits (8/8, varying from mild to severe)
o    Behavioral abnormalities / ADHD (males, 4/4)
o    Visual impairment due to cataracts (8/8)
o    Strabismus (8/8)
o    Poor visual tracking (8/8)

•    Other symptoms:
o    Sleep disturbances (5/8)
o    Bronchial asthma (5/8)
o    Small ears (5/8)
o    Clumsy, hypotonic gait (8/8)