RSPRY1

Clinical Characteristics

Mutations in the RSPRY1 gene may cause the following signs and symptoms:

  • Developmental delay
  • Delayed bone development
  • Intellectual disability
  • Speech impairment
  • Microcephaly (smaller than normal head)
  • Short stature
  • Facial dysmorphia
  • Scoliosis (sideway twisting of the spine)
  • Flattening of the vertebral bones
  • Deformity of the hips
  • Deformity of the knee joints
  • Shortened leg bones
  • Shortened foot bones causing overriding of toes
  • CT imaging of the brain may reveal an abnormality with the structure of the brain.

RSPRY1-related disorder has a very early onset: from birth or early infancy.