RTTN

Clinical Characteristics

Mutations in RTTN gene cause congenital malformations (birth defects) involving the:

Brain and central nervous system:

  • Microcephaly (smaller than normal head) and the associated problems, including seizures, developmental delay, mental retardation, facial distoration, and commonly dwarfism (short stature).
  • Decrease in the size of the brain
  • Craniosynostosis (premature fusion of the joints between the bones of an infant skull)
  • Absence or decrease in the number of normal convolutions (folds) in the brain
  • Increase in the number of folds in the brain with shallow groove
  • Seizures
  • Cognitive disabilities
  • Stiff or floppy limbs

Other organs and structures:

  • Missing one or both kidneys
  • Abnormal location of a kidney
  • Undescended testes
  • Abnormal location of the opening of the urethra, e.g. on the underside of the penis instead of at the tip.
  • Joint contractures (shortening of a joint)
  • Abnormalities in the structure of the sacrum (the lower part of the back)