SMS

Management

Given the paucity of affected individuals reported, there are currently no specific management and surveillance guidelines for Snyder-Robinson syndrome. As no cure for this condition is available yet, symptomatic treatment should be established based on the occurrence of clinical manifestations.
General advice includes:

  • Assessment by a Clinical Geneticist
  • Assessment by Neurology, as required, and symptomatic management of neurologic involvement/seizures
  • Developmental assessment
  • Referral to speech, physical and occupational therapies
  • DEXA scan for osteoporosis (note that the use of bisphosphonate for osteoporosis in Snyder-Robinson syndrome is controversial) and orthopedic evaluation for kyphoscoliosis
  • Audiology for hearing impairment
  • Genetic counselling should be made available to parents