TMEM231

Clinical Characteristics

The clinical features of Meckel-Gruber syndrome include:

  • Polycystic kidneys
  • Polydactyly (of the hands and feet)
  • Occipital encephalocele
  • Oligohydramnios
  • Early death (usually in-utero or early infancy)

The clinical features of Joubert syndrome include:

  • Oculomotor apraxia
  • Breathing abnormalities
  • Molar tooth sign on brain MRI
  • Psychomotor developmental delay
  • Lack of speech
  • Lack of ambulation
  • Other less consistent features, including:
    • Polydactyly
    • Syndactyly
    • Retinopathy
    • Aggressive behavior